The syndrome of Evans also known as syndrome anti-fosfolípide, is an autoimmune disease rare, in which the body produces antibodies that destroy the blood.
Some patients with this disease may have only the white blood cells destroyed or only the red cells, but the entire structure of the blood may be damaged, when it comes to the Syndrome of Evans.
The sooner it is done the correct diagnosis of this syndrome, the easier to control the symptoms and thus the patient has a better quality of life.
It is still unknown the factor that promotes this syndrome, and in both the symptoms such as the evolution of this rare disease are very different from case to case, depending on the portion of the blood that suffers the attack of the antibodies.
Signs and symptoms
When the red cells are damaged, lowering its blood levels, the patient develops the typical symptoms of anemia, in cases that are the platelets to be destroyed, the patient becomes more susceptible to the formation of bruises and sagramentos that in cases of head injury can cause cerebral haemorrhages fatal and when it is the white portion of the blood that is affected by the patient becomes more susceptible to infections accompanied by greater difficulty of recovery.
It is common for the patient with syndrome of Evans can present other autoimmune diseases such as lupus or rheumatoid arthritis, for example.
The evolution of the disease is unexpected and in many cases the episodes of the great destruction of blood cells are followed by long periods of remission, while some of the more severe cases evolve continuously without periods of improvement of the framework.
How is it treated
The treatment goal is to stop the production of antibodies that destroy the blood. The treatment does not cure the disease, but helps reduce your symptoms, such as anemia or thrombosis.
The use of steroids is recommended as it suppresses the immune system and decrease the production of antibodies, thereby interrupting or decreasing the degree of destruction of blood cells.
Another option is the injection of immunoglobulins to destroy the excess of antibodies produced by the body or even chemotherapy, which stabilizes the patient.